| Enzymes A-Z A B C D E F G H I J K L M N O P Q R S T U V W X Y Z Diseases 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) Name: | 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) (1.2.4.4) | Alternative Name: | 2-oxoisocaproate dehydrogenase.
2-oxoisovalerate (lipoate) dehydrogenase.
3-methyl-2-oxobutanoate dehydrogenase (lipoamide).
3-methyl-2-oxobutanoate:lipoamide oxidoreductase (decarboxylating and
acceptor-2-methylpropanoylating).
Alpha-keto-alpha-methylvalerate dehydrogenase.
Alpha-ketoisocaproate dehydrogenase.
Alpha-ketoisocaproic dehydrogenase.
Alpha-ketoisocaproic-alpha-keto-alpha-methylvaleric dehydrogenase.
Alpha-ketoisovalerate dehydrogenase.
Alpha-oxoisocaproate dehydrogenase.
BCKDH.
BCOAD.
Branched chain keto acid dehydrogenase.
Branched-chain (-2-oxoacid) dehydrogenase (BCD).
Branched-chain 2-keto acid dehydrogenase.
Branched-chain 2-oxo acid dehydrogenase.
Branched-chain alpha-keto acid dehydrogenase.
Branched-chain alpha-oxo acid dehydrogenase.
Branched-chain keto acid dehydrogenase.
Branched-chain ketoacid dehydrogenase.
Dehydrogenase, 2-oxoisovalerate (lipoate).
Dehydrogenase, branched chain alpha-keto acid.
| Structure & Reaction: | 1.2.4.4 | Details: | ExPASy, BRENDA, DBGET, PubMed, IntEnz, GO | Diseases: | Maple syrup urine disease; MIN:248600, Clinical Synopsis . | Other Resources |
KEGG,
Taxonomy of Reactions, Google |
Medical Models
Click me!
|
|