The Electronic Protocol Book Table of contents BioToolKit 300 Download Trials
     An electronic protocol book with 500 protocols and 100 recipes. A great quick and practical reference for bench scientists as well as for new students.   Get A Copy      A collection of tools frequently used by bench biomedical scientists, ranging from centrifugation force conversion, molecular weight, OD, recipe calculators, to clinical calculators. Include all Primo 3.4, Abie 3.0, Heatmap Viewer, MicroHelper, Godlist Manager, label printing, and grade book.   More info

Enzymes  A-Z A B C D E F G H I J K L M N O P Q R S T U V W X Y Z Diseases

3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring)

Name: 3-methyl-2-oxobutanoate dehydrogenase (2-methylpropanoyl-transferring) (
Alternative Name: 2-oxoisocaproate dehydrogenase. 2-oxoisovalerate (lipoate) dehydrogenase. 3-methyl-2-oxobutanoate dehydrogenase (lipoamide). 3-methyl-2-oxobutanoate:lipoamide oxidoreductase (decarboxylating and acceptor-2-methylpropanoylating). Alpha-keto-alpha-methylvalerate dehydrogenase. Alpha-ketoisocaproate dehydrogenase. Alpha-ketoisocaproic dehydrogenase. Alpha-ketoisocaproic-alpha-keto-alpha-methylvaleric dehydrogenase. Alpha-ketoisovalerate dehydrogenase. Alpha-oxoisocaproate dehydrogenase. BCKDH. BCOAD. Branched chain keto acid dehydrogenase. Branched-chain (-2-oxoacid) dehydrogenase (BCD). Branched-chain 2-keto acid dehydrogenase. Branched-chain 2-oxo acid dehydrogenase. Branched-chain alpha-keto acid dehydrogenase. Branched-chain alpha-oxo acid dehydrogenase. Branched-chain keto acid dehydrogenase. Branched-chain ketoacid dehydrogenase. Dehydrogenase, 2-oxoisovalerate (lipoate). Dehydrogenase, branched chain alpha-keto acid.
Structure & Reaction:
Details: ExPASy, BRENDA, DBGET, PubMed, IntEnz, GO
Diseases: Maple syrup urine disease; MIN:248600, Clinical Synopsis .
Other Resources KEGG, Taxonomy of Reactions, Google

Medical Models

Click me!



Copyright © 2002-2004 Chang Bioscience, Inc. All rights reserved.